From: Recurrent parvovirus B19 viremia resulting in two episodes of hemophagocytic lymphohistiocytosis
Parameter | Unit | reference values | 1st episode | follow-up | 2nd episode | follow-up | 3rd episode |
---|---|---|---|---|---|---|---|
(t0) | 2 months | 12 months | 15 months | 21 months | |||
CRP | mg/dl | < 0.5 | 12.2 | < 0.1 | 1.3 | < 0.1 | 1.5 |
PCT | ng/ml | < 0.05 | 10.38 | .. | 0.18 | .. | .. |
LDH | U/l | < 247 | 2844 | 215 | 653 | .. | 337 |
GOT (AST) | U/l | < 31 | 2635 | 17 | 105 | 15 | 31 |
Ferritin | µg/l | 13,0–150,0 | 24,068# | 179.4 | 9864# | 65.2 | 1323# |
sCD25 (sIL-2R) | kU/l | 158–623 | 3822# | .. | 1136 | .. | 490 |
White blood count | nl−1 | 4–11 | 0.6 | 4.4 | 2.6 | 10.7 | 5.8 |
Neutrophiles | nl−1 | 2.0–8.3 | 0.3# | .. | 1.2 | .. | 4.22 |
Platelets | nl−1 | 150–400 | 48# | 212 | 66# | 247 | 179 |
Hemoglobine | g/dl | 11.9–14.6 | 6.3# | 13.4 | 11.0 | 14.4 | 10.5 |
Fibrinogen | mg/dl | 210–400 | 236 | .. | 254 | .. | 401 |
Triglycerides | mg/dl | < 150 | 229 | 54 | 140 | .. | .. |
NK cell activity | .. | .. | .. | .. | .. | Normal | |
Parvovirus B19-DNA | IU/ml | Negative | 1761 | Negative | 275 | .. | 2 |
Temperature | °C | 40.4# | 39.0# | 36.6 | |||
Spleen length | mm | < 110 | 161# | 112 | 124# | 109 | |
Liver size (cc and dv in MCL) | mm | ( +) 110/167 | 112/144 | 122/128 | 131/140 | ||
Hemophagocytosis | Yes/no | No | (−)* | .. | .. | ||
HLH2004 | n | < 5 | 5 | 3 | 1 | ||
Hscore | n | 264 | 193 | 19 | |||
Corresp. likelihood | % | > 99 | 80–88 | < 1 |